UNCOMMON AURAL MASS: SPINDLE CELL VARIANT OF EMBRYONAL RHABDOMYOSARCOMA UNVEILED - A RARE CASE REPORT

Abstract

Rhabdomyosarcoma is most common soft tissue sarcoma often affects children arising from skeletal muscle. A 4-year-old girl presented with  2weeks history of left ear blood-stained purulent discharge and aural growth. CE-MRI revealed a homogeneous soft tissue lesion in the left external auditory canal extending into the middle ear and mastoid air cells. HPE confirmed the spindle cell variant of Embryonal subtype RMS, with MyoD1 and Ki67 positivity, involving the left mastoid, and treated with neoadjuvant chemotherapy, radical mastoidectomy, radiotherapy, and additional chemotherapy.This aggressive multimodal approach achieved favorable initial outcomes,with no recurrence,emphasizingearly,intensive therapy's role in localized disease control and prognosis improvement.